Chest Lectures
Pulmonary fibrosis - imaging survival guide
In this lecture, Miranda Siemienowicz breaks down everything that is known about fibrotic lung disease and summarizes the essential elements you'll need to know to report these cases day-to-day. View slides and cases
3 Review Questions
Question 1
{"accessible":false,"alternatives":[{"id":11566,"text":"any fibrotic lung disease with a honeycombing appearance should be reported as \"typical UIP\""},{"id":11567,"text":"distribution is often patchy, with interspersed regions of normal peripheral lung"},{"id":11568,"text":"distribution is predominantly in the lower zone of the lungs"},{"id":11569,"text":"there is frequently a heterogeneous degree of coarseness, with both early fibrotic changes and end-stage fibrosis represented in the same patient"}],"archived":false,"correctAlternativeId":11566,"explanation":"\u003cp\u003eAlthough honeycombing occurs most commonly in “typical \u003ca href=\"/articles/usual-interstitial-pneumonia\"\u003eUIP\u003c/a\u003e”, it can be seen in other fibrotic lung diseases as well, such as \u003ca href=\"/articles/fibrotic-hypersensitivity-pneumonitis\"\u003efibrotic hypersensitivity pneumonitis\u003c/a\u003e.\u003c/p\u003e","id":2342,"imageUrl":null,"imageAttribution":null,"imageAttributionCaseInfo":null,"firstQuestionPath":"/questions/2","nextQuestionPath":"/questions/2344","relatedArticles":[{"id":16895,"title":"Usual interstitial pneumonia","link":"/articles/usual-interstitial-pneumonia"},{"id":17181,"title":"Hypersensitivity pneumonitis","link":"/articles/hypersensitivity-pneumonitis"},{"id":11007,"title":"Non-specific interstitial pneumonia","link":"/articles/non-specific-interstitial-pneumonia-1"},{"id":43552,"title":"Idiopathic interstitial pneumonias: HRCT chest approach","link":"/articles/idiopathic-interstitial-pneumonias-hrct-chest-approach"},{"id":1431,"title":"Three attenuation pattern","link":"/articles/three-attenuation-pattern"},{"id":43571,"title":"Diagnostic HRCT criteria for usual interstitial pneumonia (UIP) pattern - ATS/ERS/JRS/ALAT (2018)","link":"/articles/diagnostic-hrct-criteria-for-usual-interstitial-pneumonia-uip-pattern-atsersjrsalat-2018"},{"id":68888,"title":"Interstitial lung abnormality","link":"/articles/interstitial-lung-abnormality"}],"alsoUsedIn":[{"id":1354,"kind":"Course","title":"2022 Virtual Conference Private Use - page 1354","link":"https://radiopaedia.org/courses/2022-virtual-conference-private-use/pages/1354"},{"id":1200,"kind":"Course","title":"2022 Virtual Conference Private Use - page 1200","link":"https://radiopaedia.org/courses/2022-virtual-conference-private-use/pages/1200"},{"id":248,"kind":"LiveSchedule","title":"248","link":"https://radiopaedia.org/admin/live_schedules/248"},{"id":168,"kind":"LiveSchedule","title":"168","link":"https://radiopaedia.org/admin/live_schedules/168"},{"id":1291,"kind":"Course","title":"2022 Virtual Conference Private Use - page 1291","link":"https://radiopaedia.org/courses/2022-virtual-conference-private-use/pages/1291"},{"id":1291,"kind":"Course","title":"Chest Lectures - page 1291","link":"https://radiopaedia.org/courses/chest-lectures/pages/1291"},{"id":1291,"kind":"Course","title":"Content Previews - page 1291","link":"https://radiopaedia.org/courses/previews/pages/1291"},{"id":1291,"kind":"Course","title":"Lecture Collections - page 1291","link":"https://radiopaedia.org/courses/lecture-collections/pages/1291"}],"stem":"\u003cp\u003eWhich of the following about usual interstitial pneumonia (UIP) is \u003cstrong\u003eFALSE\u003c/strong\u003e?\u003c/p\u003e","menuLinks":[{"text":"Report problem with question","url":"https://docs.google.com/forms/d/e/1FAIpQLSfO3soWYhOjJ7yErSysyCe5V4A1CqW7WK3rDA7MtAkecMGqNw/viewform?entry.1624461248\u0026entry.553583435=https://radiopaedia.org/questions/2342"}],"attemptsPercentages":[{"alternativeId":"11568","percentage":3},{"alternativeId":"11569","percentage":7},{"alternativeId":"11567","percentage":13},{"alternativeId":"11566","percentage":77}],"promptToLogin":false,"questionManager":false,"displayNextQuestion":false,"displaySkipQuestion":false,"displayRelatedArticles":false,"contextType":"RestrictedPage","contextId":1291,"showAsPoll":false,"showAsPollResults":false}
Question 2
{"accessible":false,"alternatives":[{"id":11574,"text":"air trapping, normal lung and ground glass densities are highly specific for the diagnosis"},{"id":11575,"text":"a pattern of fibrosis that is concordant with HP is termed \"axially diffuse\", implying both a peripheral and peribronchovascular distribution"},{"id":11576,"text":"evidence of airway involvement on CT, such as air trapping, is required as per the 2020 international clinical practice guideline for HP diagnosis"},{"id":11577,"text":"fibrotic HP commonly has an upper zone predominance"}],"archived":false,"correctAlternativeId":11577,"explanation":"\u003cp\u003eOnly a small minority of cases of \u003ca href=\"/articles/fibrotic-hypersensitivity-pneumonitis\"\u003efibrotic HP\u003c/a\u003e have a pure upper zone predominance. When present, this is a useful differentiator, but other features should be relied upon for initial interpretation.\u003c/p\u003e","id":2344,"imageUrl":null,"imageAttribution":null,"imageAttributionCaseInfo":null,"firstQuestionPath":"/questions/2","nextQuestionPath":"/questions/2345","relatedArticles":[{"id":16895,"title":"Usual interstitial pneumonia","link":"/articles/usual-interstitial-pneumonia"},{"id":17181,"title":"Hypersensitivity pneumonitis","link":"/articles/hypersensitivity-pneumonitis"},{"id":11007,"title":"Non-specific interstitial pneumonia","link":"/articles/non-specific-interstitial-pneumonia-1"},{"id":43552,"title":"Idiopathic interstitial pneumonias: HRCT chest approach","link":"/articles/idiopathic-interstitial-pneumonias-hrct-chest-approach"},{"id":1431,"title":"Three attenuation pattern","link":"/articles/three-attenuation-pattern"},{"id":43571,"title":"Diagnostic HRCT criteria for usual interstitial pneumonia (UIP) pattern - ATS/ERS/JRS/ALAT (2018)","link":"/articles/diagnostic-hrct-criteria-for-usual-interstitial-pneumonia-uip-pattern-atsersjrsalat-2018"},{"id":68888,"title":"Interstitial lung abnormality","link":"/articles/interstitial-lung-abnormality"},{"id":98325,"title":"Fibrotic hypersensitivity pneumonitis","link":"/articles/fibrotic-hypersensitivity-pneumonitis"}],"alsoUsedIn":[{"id":1354,"kind":"Course","title":"2022 Virtual Conference Private Use - page 1354","link":"https://radiopaedia.org/courses/2022-virtual-conference-private-use/pages/1354"},{"id":1200,"kind":"Course","title":"2022 Virtual Conference Private Use - page 1200","link":"https://radiopaedia.org/courses/2022-virtual-conference-private-use/pages/1200"},{"id":248,"kind":"LiveSchedule","title":"248","link":"https://radiopaedia.org/admin/live_schedules/248"},{"id":168,"kind":"LiveSchedule","title":"168","link":"https://radiopaedia.org/admin/live_schedules/168"},{"id":1291,"kind":"Course","title":"2022 Virtual Conference Private Use - page 1291","link":"https://radiopaedia.org/courses/2022-virtual-conference-private-use/pages/1291"},{"id":1291,"kind":"Course","title":"Chest Lectures - page 1291","link":"https://radiopaedia.org/courses/chest-lectures/pages/1291"},{"id":1291,"kind":"Course","title":"Content Previews - page 1291","link":"https://radiopaedia.org/courses/previews/pages/1291"},{"id":1291,"kind":"Course","title":"Lecture Collections - page 1291","link":"https://radiopaedia.org/courses/lecture-collections/pages/1291"}],"stem":"\u003cp\u003eWhich of the following is \u003cstrong\u003eFALSE\u003c/strong\u003e in fibrotic hypersensitivity pneumonitis (HP)?\u003c/p\u003e","menuLinks":[{"text":"Report problem with question","url":"https://docs.google.com/forms/d/e/1FAIpQLSfO3soWYhOjJ7yErSysyCe5V4A1CqW7WK3rDA7MtAkecMGqNw/viewform?entry.1624461248\u0026entry.553583435=https://radiopaedia.org/questions/2344"}],"attemptsPercentages":[{"alternativeId":"11575","percentage":15},{"alternativeId":"11574","percentage":11},{"alternativeId":"11577","percentage":56},{"alternativeId":"11576","percentage":17}],"promptToLogin":false,"questionManager":false,"displayNextQuestion":false,"displaySkipQuestion":false,"displayRelatedArticles":false,"contextType":"RestrictedPage","contextId":1291,"showAsPoll":false,"showAsPollResults":false}
Question 3
{"accessible":false,"alternatives":[{"id":11578,"text":"all ground glass opacities in NSIP indicate reversible disease"},{"id":11579,"text":"prone imaging is less useful in NSIP than in other forms of fibrotic lung disease"},{"id":11580,"text":"subpleural sparing can be lost in severe extent disease"},{"id":11581,"text":"true idiopathic presentation is the most common etiology"}],"archived":false,"correctAlternativeId":11580,"explanation":"\u003cp\u003e\u003ca href=\"/articles/subpleural-sparing\"\u003eSubpleural sparing\u003c/a\u003e\u0026nbsp;is best appreciated in early disease, but can be lost in severe, late stage disease. This\u0026nbsp;highlights\u0026nbsp;the critical importance of reviewing oldest available imaging when interpreting these cases.\u003c/p\u003e\u003cp\u003e\u003ca href=\"/articles/non-specific-interstitial-pneumonia-1\"\u003eNSIP\u003c/a\u003e is most commonly seen as a complication of connective tissue disease. Prone imaging is often used in the work-up as it allows accurate assessment of the disease's extent, especially when low-volume disease is common.\u0026nbsp;The finding of \u003ca href=\"/articles/ground-glass-opacification-3\"\u003eground glass opacity\u003c/a\u003e, when superimposed on \u003ca href=\"/articles/reticular-interstitial-pattern\"\u003ereticulation\u003c/a\u003e or \u003ca href=\"/articles/traction-bronchiectasis\"\u003etraction bronchiectasis\u003c/a\u003e, suggests fine fibrosis below the resolution of CT, whereas ground glass opacity distant to features of established fibrosis is likely to be reversible with treatment.\u003c/p\u003e","id":2345,"imageUrl":null,"imageAttribution":null,"imageAttributionCaseInfo":null,"firstQuestionPath":"/questions/2","nextQuestionPath":"/questions/2346","relatedArticles":[{"id":16895,"title":"Usual interstitial pneumonia","link":"/articles/usual-interstitial-pneumonia"},{"id":11007,"title":"Non-specific interstitial pneumonia","link":"/articles/non-specific-interstitial-pneumonia-1"},{"id":43552,"title":"Idiopathic interstitial pneumonias: HRCT chest approach","link":"/articles/idiopathic-interstitial-pneumonias-hrct-chest-approach"},{"id":1431,"title":"Three attenuation pattern","link":"/articles/three-attenuation-pattern"},{"id":68888,"title":"Interstitial lung abnormality","link":"/articles/interstitial-lung-abnormality"}],"alsoUsedIn":[{"id":1354,"kind":"Course","title":"2022 Virtual Conference Private Use - page 1354","link":"https://radiopaedia.org/courses/2022-virtual-conference-private-use/pages/1354"},{"id":1200,"kind":"Course","title":"2022 Virtual Conference Private Use - page 1200","link":"https://radiopaedia.org/courses/2022-virtual-conference-private-use/pages/1200"},{"id":248,"kind":"LiveSchedule","title":"248","link":"https://radiopaedia.org/admin/live_schedules/248"},{"id":168,"kind":"LiveSchedule","title":"168","link":"https://radiopaedia.org/admin/live_schedules/168"},{"id":1291,"kind":"Course","title":"2022 Virtual Conference Private Use - page 1291","link":"https://radiopaedia.org/courses/2022-virtual-conference-private-use/pages/1291"},{"id":1291,"kind":"Course","title":"Chest Lectures - page 1291","link":"https://radiopaedia.org/courses/chest-lectures/pages/1291"},{"id":1291,"kind":"Course","title":"Content Previews - page 1291","link":"https://radiopaedia.org/courses/previews/pages/1291"},{"id":1291,"kind":"Course","title":"Lecture Collections - page 1291","link":"https://radiopaedia.org/courses/lecture-collections/pages/1291"}],"stem":"\u003cp\u003eWhich of the following about non-specific interstitial pneumonia (NSIP) is true?\u003c/p\u003e","menuLinks":[{"text":"Report problem with question","url":"https://docs.google.com/forms/d/e/1FAIpQLSfO3soWYhOjJ7yErSysyCe5V4A1CqW7WK3rDA7MtAkecMGqNw/viewform?entry.1624461248\u0026entry.553583435=https://radiopaedia.org/questions/2345"}],"attemptsPercentages":[{"alternativeId":"11578","percentage":10},{"alternativeId":"11579","percentage":7},{"alternativeId":"11581","percentage":13},{"alternativeId":"11580","percentage":70}],"promptToLogin":false,"questionManager":false,"displayNextQuestion":false,"displaySkipQuestion":false,"displayRelatedArticles":false,"contextType":"RestrictedPage","contextId":1291,"showAsPoll":false,"showAsPollResults":false}
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