Blue rubber bleb nevus syndrome
Updates to Article Attributes
Blue rubber bleb nevus syndrome (BRBNS) or Bean syndrome, is a rare sporadic syndrome characterised by multifocal venous anomalies. Patients often have multiple soft blue skin lesions associated with multiple bowel venous malformations, which could lead to lower gastrointestinal bleeding.
Pathology
The skin and gastrointestinal tract are the primary sites of Involvement it can affect multiple other organ systems which include musculoskeltal system, vulva, submandibular region, parotid region, thymus, masticator space, cranium (sinus pericranii). Involvement of the orbits, thyroid, heart, pericardium, lungs, peritoneal cavity, adrenal glands, and kidneys have also been rarely reported 3.
History and etymology
The association of “haemangiomas” of the skin and gastrointestinal tract was first reported in 1860 by Gascoyen . It was fully characterised by William Bean in 1958 2.
See also
-<p><strong>Blue rubber bleb nevus syndrome (BRBNS) </strong>or <strong>Bean syndrome</strong>, is a rare sporadic syndrome characterised by multifocal venous anomalies. Patients often have multiple soft blue skin lesions associated with multiple bowel venous malformations, which could lead to <a title="Lower gastrointestinal bleeding" href="/articles/lower-gastrointestinal-bleeding">lower gastrointestinal bleeding</a>. </p><h4>Pathology</h4><p>The skin and gastrointestinal tract are the primary sites of Involvement it can affect multiple other organ systems which include musculoskeltal system, vulva, submandibular region, parotid region, thymus, masticator space, cranium (<a href="/articles/sinus-pericranii">sinus pericranii</a>). Involvement of the orbits, thyroid, heart, pericardium, lungs, peritoneal cavity, adrenal glands, and kidneys have also been rarely reported <sup>3</sup>.</p><h4>History and etymology</h4><p>The association of “haemangiomas” of the skin and gastrointestinal tract was first reported in 1860 by Gascoyen . It was fully characterised by <strong>William Bean</strong> in 1958 <sup>2</sup>.</p><h4>See also</h4><ul><li><a href="/articles/issva-classification-of-vascular-anomalies">ISSVA classification of vascular anomalies</a></li></ul>- +<p><strong>Blue rubber bleb nevus syndrome (BRBNS) </strong>or <strong>Bean syndrome</strong>, is a rare sporadic syndrome characterised by multifocal venous anomalies. Patients often have multiple soft blue skin lesions associated with multiple bowel venous malformations, which could lead to <a href="/articles/lower-gastrointestinal-bleeding">lower gastrointestinal bleeding</a>. </p><h4>Pathology</h4><p>The skin and gastrointestinal tract are the primary sites of Involvement it can affect multiple other organ systems which include musculoskeltal system, vulva, submandibular region, parotid region, thymus, masticator space, cranium (<a href="/articles/sinus-pericranii">sinus pericranii</a>). Involvement of the orbits, thyroid, heart, pericardium, lungs, peritoneal cavity, adrenal glands, and kidneys have also been rarely reported <sup>3</sup>.</p><h4>History and etymology</h4><p>The association of “haemangiomas” of the skin and gastrointestinal tract was first reported in 1860 by Gascoyen . It was fully characterised by <strong>William Bean</strong> in 1958 <sup>2</sup>.</p><h4>See also</h4><ul><li><a href="/articles/issva-classification-of-vascular-anomalies">ISSVA classification of vascular anomalies</a></li></ul>
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