Question 1797
{"accessible":true,"alternatives":[{"id":8927,"text":"Fanconi anemia "},{"id":8928,"text":"hereditary spherocytosis"},{"id":8929,"text":"iron deficiency anemia"},{"id":8930,"text":"sickle cell disease"},{"id":8931,"text":"thalassemia major"}],"archived":false,"correctAlternativeId":8927,"explanation":"\u003cp\u003eThis skull x-ray (lateral view) demonstrates the characteristic appearance of \u003cstrong\u003ehair on end sign \u003c/strong\u003ewhich is the result of the\u003cstrong\u003e\u0026nbsp;\u003c/strong\u003emanifestations of the extra-medullary hematopoiesis with\u0026nbsp;thickening of the\u0026nbsp;trabeculae running perpendicularly within a\u0026nbsp;widened\u0026nbsp;diploic space,\u0026nbsp;interspersed by radiolucent marrow hyperplasia along the skull vault.\u003c/p\u003e\u003cp\u003eThis appearance is classically described on plain skull radiographs but can also be seen on CT or MRI in patients with\u003c/p\u003e\u003cul\u003e\n\u003cli\u003e\u003cp\u003ethalassemia major\u003c/p\u003e\u003c/li\u003e\n\u003cli\u003e\u003cp\u003esickle cell disease\u003c/p\u003e\u003c/li\u003e\n\u003cli\u003e\u003cp\u003ehereditary spherocytosis\u003c/p\u003e\u003c/li\u003e\n\u003cli\u003e\u003cp\u003eiron deficiency anemia\u003c/p\u003e\u003c/li\u003e\n\u003c/ul\u003e","id":1797,"imageUrl":"https://prod-images-static.radiopaedia.org/multiple_choice_questions/286/thalassemia-2_big_gallery.jpeg","imageAttribution":{"kind":"case","rID":42141},"imageAttributionCaseInfo":{"title":"Thalassemia","contributor_name":"Melbourne Uni Radiology Masters","contributor_param":"rmhrw","case_rid":42141,"case_param":"thalassemia-2"},"firstQuestionPath":"/questions/1797","nextQuestionPath":null,"relatedArticles":[{"id":6473,"title":"Iron deficiency anemia","link":"/articles/iron-deficiency-anaemia?lang=us"},{"id":15616,"title":"Thalassemia","link":"/articles/thalassaemia?lang=us"},{"id":12457,"title":"Sickle cell disease (skeletal manifestations)","link":"/articles/sickle-cell-disease-skeletal-manifestations-1?lang=us"},{"id":67218,"title":"Hereditary spherocytosis","link":"/articles/hereditary-spherocytosis?lang=us"}],"alsoUsedIn":[],"stem":"\u003cp\u003eThe radiographic appearance seen on this skull radiograph (lateral view) has been described in patients with the following diseases \u003cstrong\u003eEXCEPT\u003c/strong\u003e one?\u003c/p\u003e","menuLinks":[{"text":"Report problem with question","url":"https://docs.google.com/forms/d/e/1FAIpQLSfO3soWYhOjJ7yErSysyCe5V4A1CqW7WK3rDA7MtAkecMGqNw/viewform?entry.1624461248\u0026entry.553583435=https://radiopaedia.org/questions/1797"}],"attemptsPercentages":[{"alternativeId":"8927","percentage":33},{"alternativeId":"8930","percentage":8},{"alternativeId":"8929","percentage":36},{"alternativeId":"8928","percentage":7},{"alternativeId":"8931","percentage":16}],"promptToLogin":false,"questionManager":false,"articleId":"fanconi-anemia"}