Hybrid nerve sheath tumor
Updates to Article Attributes
Body
was changed:
Hybrid nerve sheath tumours are uncommon, and most commonly encountered in the setting of neurofibromatosis type 1 or neurofibromatosis type 2. They represent benign peripheral nerve sheath tumours with combined histological features. The recognised combinations are 1:
- schwannoma + perineurioma (usually sporadic)
- schwannoma + neurofibroma (usually in the setting of NF1 or NF2)
- neurofibroma + perineurioma (rare, usually in the setting of NF1)
Hybrid nerve sheath tumours usually arise from peripheral nerve sheath tumours, rarely seen involving cranial nerves or spinal nerves 1.
-<p>Hybrid nerve sheath tumours </p>- +<p><strong>Hybrid nerve sheath tumours</strong> are uncommon, and most commonly encountered in the setting of <a href="/articles/neurofibromatosis-type-1">neurofibromatosis type 1</a> or <a href="/articles/neurofibromatosis-type-2-3">neurofibromatosis type 2</a>. They represent benign <a title="Peripheral nerve sheath tumours" href="/articles/peripheral-nerve-sheath-tumours">peripheral nerve sheath tumours</a> with combined histological features. The recognised combinations are <sup>1</sup>: </p><ul>
- +<li>
- +<a title="Schwannoma" href="/articles/schwannoma">schwannoma</a> + <a title="Perineurioma" href="/articles/perineurioma">perineurioma</a> (usually sporadic)</li>
- +<li>
- +<a title="Schwannoma" href="/articles/schwannoma">schwannoma</a> + <a title="Neurofibroma" href="/articles/neurofibroma">neurofibroma</a> (usually in the setting of <a title="NF1" href="/articles/neurofibromatosis-type-1">NF1</a> or <a title="NF2" href="/articles/neurofibromatosis-type-2-3">NF2</a>)</li>
- +<li>
- +<a title="Neurofibroma" href="/articles/neurofibroma">neurofibroma</a> + <a title="Perineurioma" href="/articles/perineurioma">perineurioma</a> (rare, usually in the setting of NF1)</li>
- +</ul><p>Hybrid nerve sheath tumours usually arise from peripheral nerve sheath tumours, rarely seen involving cranial nerves or spinal nerves <sup>1</sup>. </p>
References changed:
- 1. Stemmer-Rachamimov AO, Hornick JL. Hybrid nerve sheath tumour. In: WHO Classification of Tumours Editorial Board. Soft tissue and bone tumours. Lyon (France): International Agency for Research on Cancer; 2020. (WHO classification of tumours series, 5th ed.; vol. 3). <a href="https://publications.iarc.fr/Book-And-Report-Series/Who-Classification-Of-Tumours/Soft-Tissue-And-Bone-Tumours-2020">https://publications.iarc.fr</a>
Systems changed:
- Musculoskeletal
Unable to process the form. Check for errors and try again.