Osteopathia striata
Updates to Article Attributes
Body
was changed:
Osteopathia striata (also known as Voorhoeve disease) is a rare, benign dysplasia of bone, involving the epiphysis and metaphysis of tubular bones.
Epidemiology
Oseopathia striata can be found in any age group.
Clinical presentation
Osteopathia striata is typically asymptomatic, although there can be associated joint discomfort.
Pathology
Associations
There is an association with Goltz syndrome.
Variants
Radiographic features
Osteopathia striata is typically bilateral, although occasionally it can be unilateral, typically in tubular bones
Radiographically prominent vertical striations predominate in the metaphyses and epiphyses of the long bones (celery stalk metaphysis).
Differential diagnosis
The differential diagnosis includes :
- normal variation in the prominence of periarticular vertical trabeculation
- adult osteopetrosis
- enchondromatosis
- osteopoikilosis
-<p><strong>Osteopathia striata</strong> (also known as <strong>Voorhoeve disease</strong>) is a rare, benign dysplasia of bone, involving the epiphysis and metaphysis of tubular bones.</p><h4>Epidemiology</h4><p>Oseopathia striata can be found in any age group. </p><h4>Clinical presentation</h4><p>Osteopathia striata is typically asymptomatic, although there can be associated joint discomfort.</p><h4>Pathology</h4><h5>Associations</h5><p>There is an association with <a href="/articles/goltz-syndrome" title="Goltz syndrome">Goltz syndrome</a>.</p><h4>Radiographic features</h4><p>Osteopathia striata is typically bilateral, although occasionally it can be unilateral, typically in tubular bones</p><p>Radiographically prominent vertical striations predominate in the metaphyses and epiphyses of the long bones (<a href="/articles/celery-stalk-metaphysis" title="celery stalk metaphysis">celery stalk metaphysis</a>). </p><h4>Differential diagnosis</h4><p>The differential diagnosis includes :</p><ul>-<li>normal variation in the prominence of periarticular vertical trabeculation</li>-<li><a href="/articles/autosomal-dominant-osteopetrosis" title="Adult osteopetrosis">adult osteopetrosis</a></li>-<li><a href="/articles/ollier-disease" title="Enchondromatosis">enchondromatosis</a></li>-<li><a href="/articles/osteopoikilosis-2" title="Osteopoikilosis">osteopoikilosis</a></li>- +<p><strong>Osteopathia striata</strong> (also known as <strong>Voorhoeve disease</strong>) is a rare, benign dysplasia of bone, involving the epiphysis and metaphysis of tubular bones.</p><h4>Epidemiology</h4><p>Oseopathia striata can be found in any age group. </p><h4>Clinical presentation</h4><p>Osteopathia striata is typically asymptomatic, although there can be associated joint discomfort.</p><h4>Pathology</h4><h5>Associations</h5><p>There is an association with <a href="/articles/goltz-syndrome">Goltz syndrome</a>.</p><h5>Variants</h5><ul><li>
- +<a title="osteopathia striata with cranial sclerosis" href="/articles/osteopathia-striata-with-cranial-sclerosis">osteopathia striata with cranial sclerosis </a><sup>5</sup>
- +</li></ul><h4>Radiographic features</h4><p>Osteopathia striata is typically bilateral, although occasionally it can be unilateral, typically in tubular bones</p><p>Radiographically prominent vertical striations predominate in the metaphyses and epiphyses of the long bones (<a href="/articles/celery-stalk-metaphysis">celery stalk metaphysis</a>). </p><h4>Differential diagnosis</h4><p>The differential diagnosis includes :</p><ul>
- +<li>normal variation in the prominence of periarticular vertical trabeculation</li>
- +<li><a href="/articles/autosomal-dominant-osteopetrosis">adult osteopetrosis</a></li>
- +<li><a href="/articles/ollier-disease">enchondromatosis</a></li>
- +<li><a href="/articles/osteopoikilosis-2">osteopoikilosis</a></li>
References changed:
- 4. Bass HN, Weiner JR, Goldman A et-al. Osteopathia striata syndrome. Clinical, genetic and radiologic considerations. Clin Pediatr (Phila). 1980;19 (5): 369-73. <a href="http://www.ncbi.nlm.nih.gov/pubmed/6965904">Pubmed citation</a><span class="auto"></span>
Images Changes:
Image 3 X-ray (Frontal) ( create )
Unable to process the form. Check for errors and try again.