Presentation
Suspicion of CPAM on prenatal ultrasound.
Patient Data
Chest X-ray taken on the day of birth.
Central opacities. Right perihilar lucencies, more prominent (pseudocystic) in the upper zone. The differential diagnosis includes CPAM.
Chest X-ray taken at age 6 months.
Large cystic lesion in the RLL.
The upper segment of the RLL is very large and is composed of cysts of different sizes, ranging up to a diameter of 2.5 cm. The entire lesion measures 4.8 x 4.1 x 4.7 cm. Mild adjacent pleural thickening. No soft tissue component or abnormal vasculature. Small RUL atelectasis. Small atelectases in the dependent portions. Mild tracheal compression anteriorly by the brachiocephalic artery.
In summary: features consistent with CPAM.
Case Discussion
Pathology report:
Upper segment right lower lobe:
Features compatible with congenital cystic adenomatoid malformation, type I.