Arrhythmogenic right ventricular cardiomyopathy

Case contributed by Tim Luijkx , 21 Sep 2015
Diagnosis certain
Changed by Tim Luijkx, 23 Sep 2015
Hidden edits. Some edits not affecting the appearance of this case have been suppressed.

Updates to Case Attributes

Status changed from draft to published (unlisted).
Visibility changed from public to unlisted.
Published At was set to .
Body was removed:

missing series:

2k rechts video/images

korte as multislice video/images

viab korte as

viab 2k rechts

RVOT video/images

1122492 ARVC

  • -<p>missing series:</p><p>2k rechts video/images</p><p>korte as multislice video/images</p><p>viab korte as</p><p>viab 2k rechts</p><p>RVOT video/images</p><p>1122492 ARVC</p>
Presentation was added:
Known arrhythmogenic right ventricular cardiomyopathy. Doesn't have an ICD. History of VT ablation in right ventricular outflow tract.
Diagnostic Certainty was set to .

Updates to Study Attributes

Findings was added:

Body surface area: 2.11 m2.Diameters: LV: 45 mm, RV: 40 mm, septum: 10 mm.

Functional parameters:LV: EDV: 195 ml / ESV 80 ml / SV: 115 ml / EF: 59% RV: EDV: 243 ml (BSA corrected: 115 ml), was 230 ml; ESV: 142 ml/ SV: 100 ml / EF: 41% (was 47%)

Marked dyskinesia with aneurysmatic bulging of the right ventricular wall, most prominent at the apex and free wall. Normal wall motion of left ventricle. Crypt in lateral LV wall.

Delayed enhancement of basal anterior RV wall towards RVOT, apical RV and at the moderator band. Ablation scarring may cause some of this.

On T1-weighted images slight fatty change of RV free wall basally and apically. Slight subepicardial fatty change of LV posterolateral wall. 

Conclusion:

Marked wall motion abnormalities of the right ventricle with reduced function (ejection fraction 41%), findings in keeping with known ARVC.

Images Changes:

Image MRI (cine video) ( update )

Perspective was set to 4 chamber.
Specifics was set to cine video.

Image MRI (cine video) ( update )

Specifics was set to cine video.
Perspective was set to 2 chamber right.

Image MRI (cine images) ( update )

Perspective was set to 2 chamber right.
Specifics was set to cine images.
Stack was set to .
Single Or Stack Root was set to .

Image MRI (cine images) ( update )

Specifics was set to cine images.
Perspective was set to RVOT.
Stack was set to .
Single Or Stack Root was set to .

Image MRI (cine video) ( update )

Perspective was set to RVOT.
Specifics was set to cine video.

Image MRI (PSIR) ( update )

Perspective was set to 2 chamber right.
Specifics was set to PSIR.

Image MRI (PSIR) ( update )

Perspective was set to RVOT.
Specifics was set to PSIR.

Image MRI (cine video) ( update )

Specifics was set to cine video.
Perspective was set to short axis.

Image MRI (PSIR) ( update )

Perspective was set to short axis.
Specifics was set to PSIR.
Stack was set to .
Single Or Stack Root was set to .

Image MRI (cine images) ( update )

Perspective was set to short axis.
Specifics was set to cine images.
Stack was set to .
Single Or Stack Root was set to .

Image MRI (T1 BB) ( update )

Perspective was set to Axial.
Specifics was set to T1 BB.
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Single Or Stack Root was set to .

Image MRI (cine images) ( update )

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Image MRI (cine images) ( update )

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Image MRI (viability) ( update )

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Image MRI (viability) ( update )

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Image MRI (T1 BB) ( update )

Stack was set to .
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Image MRI (PSIR) ( update )

Stack was set to .
Single Or Stack Root was set to .

Image MRI (cine images) ( update )

Perspective was set to 4 chamber.
Specifics was set to cine images.

Image 3 MRI (cine video) ( create )

Image 4 MRI (cine images) ( create )

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Image 5 MRI (cine video) ( create )

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Image 6 MRI (cine images) ( create )

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Image 7 MRI (cine video) ( create )

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Image 9 MRI (cine video) ( create )

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Image 10 MRI (cine images) ( create )

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Image 11 MRI (viability) ( update )

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Image 12 MRI (PSIR) ( create )

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Image 13 MRI (PSIR) ( create )

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Image 14 MRI (PSIR) ( create )

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Image 15 MRI (T1 BB) ( create )

Position was set to .

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