Pulmonary hypertension

Case contributed by Michelle Foo , 24 Jul 2021
Diagnosis almost certain
Changed by Mostafa Elfeky, 5 Sep 2021

Updates to Case Attributes

Body was changed:

6-minute walk test revealed poor endurance, having to take frequent breaks, and desaturation down to 84% on room air. Ventilation/Perfusion scan (V/Q) excluded pulmonary emboli. Full blood examination, renal and liver function tests and autoimmune screen were all normal. Transthoracic echocardiogram found an enlarged right ventricle with impaired systolic function and estimated pulmonary artery pressure (PAP) of 67mmHg.

Right heart catheterisation recorded elevated pulmonary artery pressure of 55mmHg on average and pulmonary vascular resistance of 11.9 Woods units by thermodilution. This confirmed a diagnosis of idiopathic pulmonary hypertension.

  • -<p>6-minute walk test revealed poor endurance, having to take frequent breaks, and desaturation down to 84% on room air. <a title="Ventilation/Perfusion scan" href="articles/vq-scan-2">Ventilation/Perfusion scan</a> (V/Q) excluded pulmonary emboli. Full blood examination, renal and liver function tests and autoimmune screen were all normal. Transthoracic echocardiogram found an enlarged right ventricle with impaired systolic function and estimated <a title="Mean pulmonary artery pressure (mPAP)" href="/articles/mean-pulmonary-arterial-pressure">pulmonary artery pressure</a> (PAP) of 67mmHg.</p><p>Right heart catheterisation recorded elevated pulmonary artery pressure of 55mmHg on average and pulmonary vascular resistance of 11.9 Woods units by thermodilution. This confirmed a diagnosis of <a title="idiopathic pulmonary hypertension" href="/articles/idiopathic-pulmonary-arterial-hypertension">idiopathic pulmonary hypertension</a>.</p><p> </p><p> </p>
  • +<p>6-minute walk test revealed poor endurance, having to take frequent breaks, and desaturation down to 84% on room air. <a href="articles/vq-scan-2">Ventilation/Perfusion scan</a> (V/Q) excluded pulmonary emboli. Full blood examination, renal and liver function tests and autoimmune screen were all normal. Transthoracic echocardiogram found an enlarged right ventricle with impaired systolic function and estimated <a href="/articles/mean-pulmonary-arterial-pressure">pulmonary artery pressure</a> (PAP) of 67mmHg.</p><p>Right heart catheterisation recorded elevated pulmonary artery pressure of 55mmHg on average and pulmonary vascular resistance of 11.9 Woods units by thermodilution. This confirmed a diagnosis of <a href="/articles/idiopathic-pulmonary-arterial-hypertension">idiopathic pulmonary hypertension</a>.</p>

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