Rheumatoid arthritis-associated interstitial lung disease (UIP pattern)
Diagnosis almost certain
Disclosures
- updated 6 Dec 2022:
Nothing to disclose
Updates to Case Attributes
Diagnostic Certainty
changed from 4 to 3.
Body
was changed:
This case clearly demonstrates the signs that have been described to be more suggestive of connective tissue disorder 1 as compared to idiopathic pulmonary fibrosis (IPF) such as exuberant honeycombing sign (large, extensive honeycomb cysts involving large regions of a lobe) and anterior upper lobe sign (involvement of the anterior aspect of upper lobes with relative sparing of rest of the upper lobes). The straight edge sign (fibrosis of lower zones with sharp demarcation with normal lung in the craniocaudal plane on coronal view) is less apparent in this study.
Serum galactomannan came back positive and patient was treated for fungal infection.
-<p>This case clearly demonstrates the signs that have been described to be more suggestive of connective tissue disorder as compared to idiopathic pulmonary fibrosis (IPF) such as <em>exuberant honeycombing sign</em> (large, extensive honeycomb cysts involving large regions of a lobe) and <em>anterior upper lobe sign</em> (involvement of the anterior aspect of upper lobes with relative sparing of rest of the upper lobes). The <em>straight edge sign</em> (fibrosis of lower zones with sharp demarcation with normal lung in the craniocaudal plane on coronal view) is less apparent in this study.</p><p>Serum galactomannan came back positive and patient was treated for fungal infection.</p>- +<p>This case clearly demonstrates the signs that have been described to be more suggestive of connective tissue disorder <sup>1 </sup>as compared to idiopathic pulmonary fibrosis (IPF) such as <em>exuberant honeycombing sign</em> (large, extensive honeycomb cysts involving large regions of a lobe) and <em>anterior upper lobe sign</em> (involvement of the anterior aspect of upper lobes with relative sparing of rest of the upper lobes). The <em>straight edge sign</em> (fibrosis of lower zones with sharp demarcation with normal lung in the craniocaudal plane on coronal view) is less apparent in this study.</p><p>Serum galactomannan came back positive and patient was treated for fungal infection.</p>
References changed:
- 1. Chung J, Cox C, Montner S et al. CT Features of the Usual Interstitial Pneumonia Pattern: Differentiating Connective Tissue Disease–Associated Interstitial Lung Disease From Idiopathic Pulmonary Fibrosis. AJR Am J Roentgenol. 2018;210(2):307-13. <a href="https://doi.org/10.2214/ajr.17.18384">doi:10.2214/ajr.17.18384</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/29140119">Pubmed</a>
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