Congenital aural atresia
This patient has had left external auditory canal atresia and conductive hearing loss since birth. This HRCT temporal bone performed is for pre-surgical planning.
The Yeakley and Jahrsdoerfer 2 grading system is useful for the pre-operative HRCT temporal bone to decide the operation's outcome. This grading system is based on nine high-resolution CT scan parameters:
normal stapes
open oval window
middle ear space
facial nerve position
malleus-incus complex
mastoid pneumatization
incus-stapes connection
open round window
external ear appearance (external auditory canal)
Each parameter is assigned 1 point (if normal or mildly dysplastic), except for the stapes which was allocated 2 points. Total 10 points.
Points (5 or below) - not a surgical candidate.
8 points and above - good surgical outcome.
7 points - fair outcome.
6 points - marginal improvement.
Our patient scored 8 points (deduct facial nerve position and external ear appearance).