Question 1546
{"accessible":false,"alternatives":[{"id":7717,"text":"20%"},{"id":7718,"text":"40%"},{"id":7719,"text":"60%"},{"id":7720,"text":"80%"}],"archived":false,"correctAlternativeId":7720,"explanation":"\u003cp\u003e80% of renal angiomyolipomas are sporadic.\u0026nbsp;The remaining 20% are seen in association with\u0026nbsp;\u003ca href=\"https://radiopaedia.org/articles/phakomatoses?lang=gb\"\u003ephakomatoses\u003c/a\u003e, the vast majority in the setting of\u0026nbsp;\u003ca href=\"https://radiopaedia.org/articles/tuberous-sclerosis?lang=gb\"\u003etuberous sclerosis\u003c/a\u003e\u0026nbsp;(80% of them get AML)\u0026nbsp;although they have also been described in the setting of\u0026nbsp;\u003ca href=\"https://radiopaedia.org/articles/von-hippel-lindau-disease-5?lang=gb\"\u003evon Hippel-Lindau syndrome (vHL)\u003c/a\u003e\u0026nbsp;and\u0026nbsp;\u003ca href=\"https://radiopaedia.org/articles/neurofibromatosis-type-1?lang=gb\"\u003eneurofibromatosis type 1 (NF1)\u003c/a\u003e.\u0026nbsp;\u003c/p\u003e","id":1546,"imageUrl":null,"imageAttribution":null,"imageAttributionCaseInfo":null,"firstQuestionPath":"/questions/2140","nextQuestionPath":"/articles/tuberous-sclerosis/questions/1346","relatedArticles":[{"id":34923,"title":"Neurofibromatosis","link":"/articles/neurofibromatosis?lang=us"},{"id":8212,"title":"Phakomatoses","link":"/articles/phakomatoses-1?lang=us"},{"id":899,"title":"Renal angiomyolipoma","link":"/articles/renal-angiomyolipoma?lang=us"},{"id":9186,"title":"Von Hippel-Lindau disease","link":"/articles/von-hippel-lindau-disease-5?lang=us"}],"alsoUsedIn":[{"id":624,"kind":"Course","title":"Radiopaedia 2020 - Lectures Only - page 624","link":"https://radiopaedia.org/courses/radiopaedia-2020-exclusive/pages/624"},{"id":624,"kind":"Course","title":"2020 Virtual Conference Private Use - page 624","link":"https://radiopaedia.org/courses/2020-virtual-conference-private-use/pages/624"},{"id":686,"kind":"Course","title":"Abdominal Emergency Radiology Course - page 686","link":"https://radiopaedia.org/courses/abdominal-emergency-radiology-course-online/pages/686"},{"id":686,"kind":"Course","title":"2020 Virtual Conference Private Use - page 686","link":"https://radiopaedia.org/courses/2020-virtual-conference-private-use/pages/686"}],"stem":"\u003cp\u003eWhat proportion of renal angiomyolipomas are sporadic in origin?\u003c/p\u003e","menuLinks":[{"text":"Report problem with question","url":"https://docs.google.com/forms/d/e/1FAIpQLSfO3soWYhOjJ7yErSysyCe5V4A1CqW7WK3rDA7MtAkecMGqNw/viewform?entry.1624461248\u0026entry.553583435=https://radiopaedia.org/questions/1546"}],"attemptsPercentages":[{"alternativeId":"7717","percentage":21},{"alternativeId":"7720","percentage":48},{"alternativeId":"7718","percentage":16},{"alternativeId":"7719","percentage":15}],"promptToLogin":false,"questionManager":false,"articleId":"tuberous-sclerosis"}