Cardiomyopathy (WHO/ISFC 1995 classification)

Changed by Jayanth Keshavamurthy, 23 Nov 2017

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Cardiomyopathy classification separates the various cardiomyopathies into several subtypes. A cardiomyopathy is defined as a "disease of the myocardium with associated cardiac dysfunction".

It was initially classified according to the 1995 WHO/ISFC system as follows:

dilated cardiomyopathy
hypertrophic cardiomyopathy
restrictive cardiomyopathy
arrhythmogenic right ventricular cardiomyopathy
specific cardiomyopathy
nonclassified cardiomyopathies which include
- fibroelastosis
- mildly dilated cardiomyopathy
- non-compacted myocardium
- mitochondrial cardiomyopathy

This has since been revised as follows ¹¹

primary cardiomyopathies predominantly involving the heart
- genetic
  - hypertrophic cardiomyopathy
  - left ventricular noncompaction
  - cardiomyopathy from glycogen storage diseases (PRKAG 2, Danon)
  - cardiomyopathy from conduction defects
  - cardiomyopathies from mitochondrial myopathies
  - cardiomyopathies from ion channel disorders (LQTS, Brugada,CVPT, Asian SUNDS)
- mixed
  - dilated cardiomyopathy
  - restrictive cardiomyopathy
- acquired
  - inflammatory
  - stress induced - Takotsubo cardiomyopathy
  - cardiomyopathy in peripartum
  - tachycardia-induced cardiomyopathy
  - cardiomyopathy in infants of diabetic mothers
secondary cardiomyopathies (these conditions can have multi-organ involvement)
- infiltrative conditions - cardiomyopathy from
- cardiomyopathy from storage conditions
  - cardiomyopathy in haemochromatosis
  - Fabry disease
  - glycogen storage disease (e.g. type II, Pompe
  - Niemann-Pick disease
- cardiomyopathy from toxic agents
  - drugs, heavy metals, chemicals
- cardiomyopathy from endomyocardial causes
  - endomyocardial fibrosis
  - Loeffler endocarditis
- cardiomyopathy from systemic inflammatory conditions
  - cardiac sarcoidosis
- cardiomyopathy from underlying systemic auto-immune conditions
- cardiomyopathy from endocrine conditions
- cardiomyopathy from neuromuscular conditions
- cardiomyopathy from underlying nutritional conditions
- cardiomyopathy from underlying electrolyte imbalances
  - potassium
  - magnesium
  - phosphate
- cardiomyopathy related to cancer treatment

~~-<li><a href="/articles/arrhythmogenic-right-ventricular-dysplasia">arrhythmogenic right ventricular cardiomyopathy</a></li>~~
+<li><a href="/articles/arrhythmogenic-right-ventricular-cardiomyopathy">arrhythmogenic right ventricular cardiomyopathy</a></li>

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