Cardiomyopathy (WHO/ISFC 1995 classification)

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Cardiomyopathy classification separates the various cardiomyopathies into several subtypes. Cardiomyopathy is defined as a "disease of the myocardium with associated cardiac dysfunction".

It was initially classified according to the 1995 World Health Organisation / International Society and Federation of Cardiology(WHO/ISFC) system as follows:

dilated cardiomyopathy
hypertrophic cardiomyopathy
restrictive cardiomyopathy
arrhythmogenic right ventricular cardiomyopathy
specific cardiomyopathy
non-classified cardiomyopathies which include
- fibroelastosis
- mildly dilated cardiomyopathy
- non-compacted myocardium
- mitochondrial cardiomyopathy

This has since been revised in 2006 by the American Heart Association (AHA) as follows ²:

primary cardiomyopathies predominantly involving the heart
- genetic
  - hypertrophic cardiomyopathy
    - cardiomyopathy from primary cardiac glycogen storage diseases (PRKAG2 cardiac syndrome, Danon disease)
  - arrhythmogenic right ventricular cardiomyopathy
  - left ventricular non-compaction
  - cardiomyopathy from conduction defects
  - cardiomyopathies from ion channelopathies (e.g. long QT syndrome, Brugada syndrome, catecholaminergic polymorphic ventricular tachycardia, short QT syndrome)
  - cardiomyopathies from mitochondrial myopathies
- mixed
  - dilated cardiomyopathy
  - restrictive cardiomyopathy
- acquired
  - inflammatory cardiomyopathy (i.e. myocarditis)
  - stress-induced cardiomyopathy (i.e. Takotsubo cardiomyopathy)
  - cardiomyopathy in peripartum and postpartum cardiomyopathy
  - tachycardia-induced cardiomyopathy
  - cardiomyopathy in infants of diabetic mothers
secondary cardiomyopathies (these conditions can have multi-organ involvement)
- infiltrative conditions - cardiomyopathy from
- cardiomyopathy from storage conditions
  - cardiomyopathy in haemochromatosis
  - Fabry disease
  - systemic glycogen storage disease (e.g. Pompe disease)
  - Niemann-Pick disease
- cardiomyopathy from toxic agents
  - drugs, heavy metals, chemicals
- cardiomyopathy from endomyocardial causes
  - endomyocardial fibrosis
  - Loeffler endocarditis
- cardiomyopathy from systemic inflammatory conditions
  - cardiac sarcoidosis
- cardiomyopathy from underlying systemic autoimmune conditions
- cardiomyopathy from endocrine conditions
- cardiomyopathy from neuromuscular conditions
- cardiomyopathy from underlying nutritional conditions
- cardiomyopathy from underlying electrolyte imbalances
  - potassium
  - magnesium
  - phosphate
- cardiomyopathy related to cancer treatment

~~-<a href="/articles/cardiomyopathy-in-peripartum">cardiomyopathy in peripartum</a> and<a href="/articles/peri-partumpost-partum-cardiomyopathy"> post-partum cardiomyopathy</a>~~
+<a href="/articles/cardiomyopathy-in-peripartum">cardiomyopathy in peripartum</a> and<a href="/articles/peripartumpostpartum-cardiomyopathy-1"> postpartum cardiomyopathy</a>
~~-<li><a title="Beriberi" href="/articles/thiamine-deficiency">beriberi</a></li>~~
+<li><a href="/articles/thiamine-deficiency">beriberi</a></li>

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Cardiomyopathy (WHO/ISFC 1995 classification)

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