This case illustrates a number of Imaging-specific features highlighted in the American College of Rheumatology (ACR) and European League Against Rheumatism (EULAR) classification criteria for IgG4-related disease with the abdomen.

Pancreas and biliary tree

• diffuse pancreatic enlargement (loss of lobulation) usually encompassing >2/3 of the pancreas

• pancreas (either of the above) and biliary tree involvement (typically proximal biliary tract)

Renal

• bilateral renal cortex low-density areas

Retroperitoneum

• diffuse thickening of the abdominal aortic wall

• circumferential or anterolateral soft tissue around the infrarenal aorta or iliac arteries