Presentation
G2P1 was sent to our institution for a routine fetal well-being scan.
Patient Data
A four-chamber view of the fetal heart shows a septum dividing the right atrium into two chambers.
Color Doppler shows flow in the right atrium of the ventricular systole with a clearly visualized septum.
Case Discussion
Cor triatriatum dextrum is a very rare congenital anomaly of the heart, accounting for 0.1% of all congenital heart defects. It is supposed to result from the persistence of the valve of sinus venous 1. During normal development, this valve regresses by 12 weeks of gestation and leaves behind the Eustachian valve, Thebesian valve, and crista terminalis. As a result of the failure of this regression, a boundary is formed between the myocardium and the trabeculated portion of the right atrium 2.
Unlike the cor triatriatum sinistrum, it has varied clinical presentations depending on the fenestration of the septum. It can be associated with an atrial septal defect, tricuspid valve abnormalities, and Ebstein anomaly 3.
Treatment of cor triatriatum dextrum depends upon the clinical symptoms and may be conservative or surgical resection of the septum 4.
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