Craniocervical junction hemangioblastoma

Case contributed by Bahman Rasuli
Diagnosis almost certain

Presentation

Familial history of von Hippel Lindau syndrome.

Patient Data

Age: 60 years
Gender: Male

18*24*36 mm cystic mass located posteriorly at the craniocervical junction. The larger non-enhancing cystic component which is present anterosuperiorly with a small and intensely enhancing nodule located posteroinferiorly abutting the pia mater. 

The cystic component appears intra-axial and separate from the fourth ventricle.

The medulla is compressed anteriorly with effacement of the premedullary cistern.  

A few abnormal foci of enhancement also is seen at the right and left cerebellar hemispheres.

Case Discussion

Although the location is unusual (and probably arises from the medulla), the imaging features are fairly typical for hemangioblastoma.

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.