Dermatofibrosarcoma protuberans

Case contributed by Binyam Tadesse Regassa
Diagnosis almost certain

Presentation

Multiple abdominal wall painless nodules and left side body weakness

Patient Data

Age: 40 years
Gender: Male

Soft tissue masses in the anterior abdominal wall, above and to the right of the umbilicus. The largest measures 5.8 cm x 2.84 cm. These masses have a uniform density and show contrast enhancement. Several smaller adjacent cutaneous nodules. No signs of internal necrosis, cystic components, or calcification.

Coarse, calcified right diaphragmatic pleural plaque.

Case Discussion

A 40-year-old man was admitted to the hospital with left sided hemiparesis and a painless abdominal wall mass.

A brain CT scan (not included) revealed an acute ischemic infraction in the left MCA territory.
An abdominal CT scan showed well-defined, homogenously enhancing masses and nodules in the subcutaneous fat of his abdomen, some of which extended to the skin surface.

A biopsy from the largest abdominal wall mass showed it to be a slow-growing, low-grade cutaneous fibrosarcoma consistent with dermatofibrosarcoma protuberans.

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