Diastematomyelia

Case contributed by Sepehr Haghighi
Diagnosis certain

Presentation

Limping

Patient Data

Age: 16 months
Gender: Male
mri

A bony spur at L1-L2 level is seen which has caused two hemicords.

Tethered cord is notable that cords have been terminated at L3 vertebral body level.

No hydromyelia is detected.

Case Discussion

Diastematomyelia, also known as a split cord malformation, refers to a type of spinal dysraphism (spina bifida occulta) when there is a longitudinal split in the spinal cord.

Classification

Split cord malformations are divided into two types according to the presence of a dividing septum and single vs dual dural sac:

  • type I: duplicated dural sac, with common midline spur (osseous or fibrous) and usually symptomatic
  • type II: single dural sac containing both hemicords; impairment less marked

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