Presentation
Male that starts with seizures of 6 years of evolution and psychomotor retardation.
Patient Data
At the supratentorial level, left hemisphere asymmetry is observed. It is smaller than the right with cerebral atrophy, associated with thickening of the left frontal and parietal bone diploe, in addition to the prominence of the arachnoid space and central, superior temporal, insular, and parietooccipital sulci. Associated retraction of the left lateral ventricle is observed prominently in all its portions, with a gliosis zone at this level.
Case Discussion
The case presented coincides with the radiological and clinical findings observed in patients with Dyke-Davidoff-Masson syndrome. This syndrome is considered a rare condition that is usually diagnosed in childhood; however, on some occasions, unilateral cerebral hemiatrophy may go unnoticed if the patient does not present clinical signs.