Dyke-Davidoff-Masson syndrome

Case contributed by Daniel De la Garza
Diagnosis certain

Presentation

Male that starts with seizures of 6 years of evolution and psychomotor retardation.

Patient Data

Age: 15 years
Gender: Male
mri

At the supratentorial level, left hemisphere asymmetry is observed. It is smaller than the right with cerebral atrophy, associated with thickening of the left frontal and parietal bone diploe, in addition to the prominence of the arachnoid space and central, superior temporal, insular, and parietooccipital sulci. Associated retraction of the left lateral ventricle is observed prominently in all its portions, with a gliosis zone at this level.

Case Discussion

The case presented coincides with the radiological and clinical findings observed in patients with Dyke-Davidoff-Masson syndrome. This syndrome is considered a rare condition that is usually diagnosed in childhood; however, on some occasions, unilateral cerebral hemiatrophy may go unnoticed if the patient does not present clinical signs.

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