Focal diastematomyelia with tethered cord

Case contributed by Sam Digby
Diagnosis almost certain

Presentation

Longstanding suspected monoplegic cerebral palsy affecting left lower limb. Left lower limb shortening and abnormal reflexes.

Patient Data

Age: 12 years
Gender: Male

There is a small focal syrinx in the distal cord at the L1/2 intervertebral disc level, associated with a split cord at the L1/2 intervertebral disc level.

There is no associated bony bar, nor an underlying mass lesion.

The conus medullaris is located at the level of the L2/3 intervertebral disc. The lumbar thecal sac and cistern are expanded.

Incidental note of flow artefact posterior to the thoracic spinal cord.

Case Discussion

There is focal diastematomyelia in the distal spinal cord and an associated small syrinx. This likely represents at type II split cord, as there appears to be a single dural sac containing both hemicords.

The low position of the conus is consistent with a tethered cord.

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.