Presentation
Primary amenorrhea.
Patient Data
Age: 25 years
Gender: Female
From the case:
Mayer-Rokitansky-Küster-Hauser syndrome (MRKH)
{"current_user":null,"step_through_annotations":true,"access":{"can_edit":false,"can_download":true,"can_toggle_annotations":true,"can_feature":false,"can_examine_pipeline_reports":false,"can_pin":false},"extraPropsURL":"/studies/111390/annotated_viewer_json?lang=us"}
Congenital absence of the uterus and upper 2/3 vagina. Both ovaries are normal in size, containing numerous small follicles.
Normal appearance and location of both kidneys on coronal T2 sequence.
Case Discussion
Case of Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) atypical form (type A) which is characterized by a congenital absence of the uterus and upper 2/3 vagina with normal ovaries and fallopian tubes and no associated renal anomalies.