Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) with rudimentary uterine horns
Presentation
Primary amenorrhea.
Patient Data
Congenital absence of the uterus and upper 2/3 vagina.
Both ovaries are normal in size, containing numerous small follicles.
Two rudimentary uterine horns connected by a thin horizontal fibrotic band well-demonstrated on axial and coronal T2 sequences.
Minimal effusion in Douglas pouch (physiological).
Normal appearance and location of both kidneys on coronal T2 sequence.
Annotated images:
red arrows; indicate the rudimentary uterine horns
green arrow: indicates the horizontal fibrotic band connecting both rudimentary horns
Case Discussion
Case of Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) with bilateral rudimentary uterine horns (rare form) class U5aC4V4 according to ESHRE/ESGE classification of female genital tract anomalies.
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