Pulmonary Langerhan’s cell histiocytosis

Case contributed by Rob Foley
Diagnosis probable

Presentation

Recent weight loss. Smoker with chronic cough.

Patient Data

Age: 50 years
Gender: Male

Widespread abnormal lung architecture with relative basal sparing and normal lung volume.

The patient subsequently presented to the emergency department with pleuritic chest pain and collapse.

New slim left apical pneumothorax. Otherwise stable appearnces

Bilateral bizarre shaped cysts with architectural distortion and relative sparing of the lung bases, in keeping with pulmonary Langerhan's cell histiocytosis (PLCH).

Slim left sided pneumothorax with multiple septations within.

There was no pulmonary embolus (vascular windows not shown).

Case Discussion

The patient's pneumothorax resolved spontaneously. Pneumothorax is a common complication of PLCH.

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