This case came for a check-up by Ultrasound and incidentally, discovered a predominantly hyperechoic mass, mostly related to the right kidney, then the CT showed a classic type of renal angiomyolipoma (AML) and the mass was excised ( subjected to total nephrectomy ) to prevent the risk of bleeding and to exclude other possibilities such as retroperitoneal liposarcoma. The histopathology showed typical (triphasic) renal angiomyolipoma (AML). Follow-up has also shown it almost stable for 10 years. 

Renal AML is the most prevalent benign neoplasm of the kidney. It has a variable and heterogeneous nature, with the potential to pose serious diagnostic challenges in clinical practice. The characteristics of classic AMLs are well described. Knowledge of the different types, their classification, and their radiologic appearance will help radiologists in making a correct diagnosis.